NADH-ubiquinone oxidoreductase chain 5

Summary
UniProt ID
P03915
Gene Symbol
  • MT-ND5
  • MTND5
  • NADH5
  • ND5
Gene ID
[4540]
Organism
Homo sapiens (human)
GlyGen
P03915
PubChem
P03915
The Human Metabolome Database
HMDBP00139
RaftProt
P03915
Re-Glyco
P03915
Annotation
Keyword
3D-structure Disease variant Leber hereditary optic neuropathy Leigh syndrome MELAS syndrome Mitochondrion inner membrane NAD Proteomics identification Reference proteome Respiratory chain Translocase Transmembrane helix Ubiquinone
Gene Ontology (GO)
GO Hierarchy
Sequence
MTMHTTMTTLTLTSLIPPILTTLVNPNKKNSYPHYVKSIVASTFIISLFPTTMFMCLDQEVIISNWHWATTQTTQLSLSFKLDYFSMMFIPVALFVTWSIMEFSLWYMNSDPNINQFFKYLLIFLITMLILVTANNLFQLFIGWEGVGIMSFLLISWWYARADANTAAIQAILYNRIGDIGFILALAWFILHSNSWDPQQMALLNANPSLTPLLGLLLAAAGKSAQLGLHPWLPSAMEGPTPVSALLHSSTMVVAGIFLLIRFHPLAENSPLIQTLTLCLGAITTLFAAVCALTQNDIKKIVAFSTSSQLGLMMVTIGINQPHLAFLHICTHAFFKAMLFMCSGSIIHNLNNEQDIRKMGGLLKTMPLTSTSLTIGSLALAGMPFLTGFYSKDHIIETANMSYTNAWALSITLIATSLTSAYSTRMILLTLTGQPRFPTLTNINENNPTLLNPIKRLAAGSLFAGFLITNNISPASPFQTTIPLYLKLTALAVTFLGLLTALDLNYLTNKLKMKSPLCTFYFSNMLGFYPSITHRTIPYLGLLTSQNLPLLLLDLTWLEKLLPKTISQHQISTSIITSTQKGMIKLYFLSFFFPLILTLLLIT
Glycosylation Sites
Displaying 1 entry
Position Description PubMed ID GlyTouCan ID Source
241
Feature
  • ProtVista GlyGen : Glycosylation Site from GlyGen
  • ProtVista UniProt : Glycosylation Site from UniProt
Pathway
Displaying all 4 entries
Pathway Name Organism
Complex I biogenesis Homo sapiens
Mitochondrial protein degradation Homo sapiens
Mitochondrial translation termination Homo sapiens
Respiratory electron transport Homo sapiens
Disease
Displaying all 3 entries
DO ID Disease Name Source
DOID:3652 Leigh disease
DOID:705 Leber hereditary optic neuropathy
DOID:3687 MELAS syndrome

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International Collaboration

GlyCosmos is a member of the GlySpace Alliance together with GlyGen and Glycomics@ExPASy.

Acknowledgements

Supported by JST NBDC Grant Number JPMJND2204

Partly supported by NIH Common Fund Grant #1U01GM125267-01


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Last updated: April 6, 2026