Pyruvate dehydrogenase protein X component, mitochondrial

Summary
UniProt ID
Q8BKZ9
Gene Symbol
  • Pdhx
Gene ID
27402
Organism
Mus musculus (house mouse)
GlyGen
Q8BKZ9
PubChem
Q8BKZ9
Re-Glyco
Q8BKZ9
Annotation
Keyword
  • Acetylation
  • Lipoyl
  • Mitochondrion
  • Phosphoprotein
  • Reference proteome
  • Transit peptide
Gene Ontology (GO)
Subcellular Location(GO Annotation)

Subcellular in which this glycoprotein is expressed are highlighted in blue.

Sequence
MAASWRLHCNQPLLRYLLGFSSRRSLGLAQGAAAWPVDRGASWRWFHSTQLLQADPIKVLMPSLSPTMEQGNIVKWLRKEGEAVSAGDSLCEIETDKAVVTLDANDDGILAKIVVEEGAKNIQLGSLIALMVEEGEDWKQVEIPKDVSAPPPVSKPPAPTQPSPQPQIPCPARKEHKGTARFRLSPAARNILEKHSLDASQGTATGPRGIFTKEDALKLVELKQMGKITESRPASAPPPSLSASVPPQATAGPSYPRPMTPPVSIPGQPNAAGTFTEIPASNIRRVIAKRLTESKSTVPHAYATADCDLGAVLKVRRDLVKDDIKVSVNDFIIRAAAVTLKQMPGVNVTWDGEGPKQLPSVDISVAVATDKGLITPIIKDAAAKGIQEIADSVKVLSKKARDGKLMPEEYQGGSFSISNLGMFGIDEFAAVINPPQACILAVGRFRPVLKLTEDEEGNPQLQQHQLITVTMSSDSRVVDDELATRFLETFKANLENPMRLG
Glycosylation Sites
Displaying all 2 entries
Position Description PubMed ID GlyTouCan ID Source
160
260
Feature
  • ProtVista GlyGen : Glycosylation Site from GlyGen
  • ProtVista UniProt : Glycosylation Site from UniProt
Pathway
Displaying all 3 entries
Pathway Name Organism
PDH complex synthesizes acetyl-CoA from PYR Mus musculus
Regulation of pyruvate dehydrogenase (PDH) complex Mus musculus
Signaling by Retinoic Acid Mus musculus

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International Collaboration

GlyCosmos is a member of the GlySpace Alliance together with GlyGen and Glycomics@ExPASy.

Acknowledgements

Supported by JST NBDC Grant Number JPMJND2204

Partly supported by NIH Common Fund Grant #1U01GM125267-01


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Last updated: December 8, 2025