Carbamoyl-phosphate synthase [ammonia], mitochondrial
| GO Term | Evidence Code | Reference |
|---|---|---|
| urea cycle | ||
| urea cycle | ||
| urea cycle | ||
| 'de novo' pyrimidine nucleobase biosynthetic process | ||
| L-glutamine metabolic process |
| GO Term | Evidence Code | Reference |
|---|---|---|
| carbamoyl-phosphate synthase (ammonia) activity | ||
| carbamoyl-phosphate synthase (ammonia) activity | ||
| carbamoyl-phosphate synthase (ammonia) activity | ||
| carbamoyl-phosphate synthase (ammonia) activity | ||
| carbamoyl-phosphate synthase (glutamine-hydrolyzing) activity |
| Position | Description | PubMed ID | GlyTouCan ID | Source |
|---|---|---|---|---|
| 22 |
|
|||
| 109 |
|
|||
| 110 |
|
|||
| 385 |
|
|
||
| 537 |
|
|||
| 861 |
|
|||
| 872 |
|
|||
| 1078 |
|
|||
| 1331 |
|
|||
| 1332 |
|
| Pathway Name | Organism |
|---|---|
| Urea cycle | Mus musculus |
| DO ID | Disease Name | Source |
|---|---|---|
| DOID:9280 | carbamoyl phosphate synthetase I deficiency disease |
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Supported by JST NBDC Grant Number JPMJND2204
Partly supported by NIH Common Fund Grant #1U01GM125267-01
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Last updated: April 6, 2026