Complex I assembly factor ACAD9, mitochondrial

Summary
UniProt ID
Q8JZN5
Gene Symbol
Acad9
Gene ID
229211
Organism
Mus musculus (house mouse)
GlyGen
Q8JZN5
PubChem
Q8JZN5
Re-Glyco
Q8JZN5
Annotation
Keyword
Acetylation FAD Mitochondrion inner membrane Oxidoreductase Phosphoprotein Reference proteome Transit peptide
Gene Ontology (GO)
GO Hierarchy
Sequence
MSGCVLLSRGATAAAAAARASRVLREFTARRRPLHTSLQSCSFAKELFLGNIEQKGVFPFPEVSQHELSEINQFVGPLEKFFTEEVDSRKIDQEGKIPVDTLEKLKSLGLFGIQVPEEYGGLGLSNTMYARLGEIISLDASITVTLAAHQAIGLKGIILVGNEEQKAKYLPKLSSGEHIAAFCLTEPASGSDAASIQTRATLSEDKKYFILNGSKVWITNGGLANIFTVFAKTEVVDSDGSKTDKMTAFIVERDFGGITNGKPEDKLGIRGSNTCEVHFENTRVPVENVLGEVGGGFKVAMNILNSGRFSMGSAVAGMLKKLIELTAEYACTRKQFNRNLSEFGLIQEKFALMAQKAYVMESMAYLTSGMLDQPGFPDCSIEAAMVKVFSSEAAWQCVSEALQILGGSGYMKDYPYERMLRDARILLIFEGTNEILRLFIALTGLQHAGRILTSRIKELKSGNVTTVMETIGRKLRDSLGRTVDLGLTGDLGVVHPSLGDSANKLEENVHYFGRTVETLLLRFGKNIVEEQLVLKRVANILINLYGMTAVLSRASRSIRIGLRNHDHEVLLANMFCVEAYFQNLFSLSQLDKNAPENLDEQIKKVSRQILEKRAYICAHPLDRAS
Glycosylation Sites
Displaying 1 entry
Position Description PubMed ID GlyTouCan ID Source
463
Feature
  • ProtVista GlyGen : Glycosylation Site from GlyGen
  • ProtVista UniProt : Glycosylation Site from UniProt
Pathway
Displaying 1 entry
Pathway Name Organism
Complex I biogenesis Mus musculus
Disease
Displaying 1 entry
DO ID Disease Name Source
DOID:0112072 nuclear type mitochondrial complex I deficiency 20

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International Collaboration

GlyCosmos is a member of the GlySpace Alliance together with GlyGen and Glycomics@ExPASy.

Acknowledgements

Supported by JST NBDC Grant Number JPMJND2204

Partly supported by NIH Common Fund Grant #1U01GM125267-01


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Last updated: April 6, 2026