Adenosine deaminase

Summary
UniProt ID
P00813
Gene Symbol
ADA ADA1
Gene ID
100
Organism
Homo sapiens (human)
PubChem
P00813
The Human Metabolome Database
HMDBP00664
The O-GlcNAc Database
P00813
RaftProt
P00813
Re-Glyco
P00813
Annotation
Keyword
3D-structure Acetylation Cell adhesion Cell junction Cell membrane Cytoplasm Cytoplasmic vesicle Direct protein sequencing Disease variant Hereditary hemolytic anemia Hydrolase Lysosome Metal-binding Nucleotide metabolism Proteomics identification Reference proteome SCID Zinc
Gene Ontology (GO)
GO Hierarchy
Sequence
MAQTPAFDKPKVELHVHLDGSIKPETILYYGRRRGIALPANTAEGLLNVIGMDKPLTLPDFLAKFDYYMPAIAGCREAIKRIAYEFVEMKAKEGVVYVEVRYSPHLLANSKVEPIPWNQAEGDLTPDEVVALVGQGLQEGERDFGVKARSILCCMRHQPNWSPKVVELCKKYQQQTVVAIDLAGDETIPGSSLLPGHVQAYQEAVKSGIHRTVHAGEVGSAEVVKEAVDILKTERLGHGYHTLEDQALYNRLRQENMHFEICPWSSYLTGAWKPDTEHAVIRLKNDQANYSLNTDDPLIFKSTLDTDYQMTKRDMGFTEEEFKRLNINAAKSSFLPEDEKRELLDLLYKAYGMPPSASAGQNL
Glycosylation Sites
Displaying 1 entry
Position Description PubMed ID GlyTouCan ID Source
358
Feature
  • ProtVista GlyGen : Glycosylation Site from GlyGen
  • ProtVista UniProt : Glycosylation Site from UniProt
Pathway
Displaying all 3 entries
Pathway Name Organism
Defective ADA disrupts (deoxy)adenosine deamination Homo sapiens
Purine salvage Homo sapiens
Ribavirin ADME Homo sapiens

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Acknowledgements

Supported by JST NBDC Grant Number JPMJND2204

Partly supported by NIH Common Fund Grant #1U01GM125267-01


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Last updated: April 6, 2026