Arylsulfatase A

Summary
UniProt ID
P50428
Gene Symbol
Arsa As2
Gene ID
11883
Organism
Mus musculus (house mouse)
GlyConnect
GlyGen
P50428
PubChem
P50428
SwissLipids
Re-Glyco
P50428
Annotation
Keyword
Calcium Disulfide bond Endoplasmic reticulum Glycoprotein Hydrolase Lipid metabolism Lysosome Metal-binding Reference proteome Signal
Gene Ontology (GO)
Sequence
MALGTLFLALAAGLSTASPPNILLIFADDLGYGDLGSYGHPSSTTPNLDQLAEGGLRFTDFYVPVSLCTPSRAALLTGRLPVRSGMYPGVLGPSSQGGLPLEEVTLAEVLAARGYLTGMAGKWHLGVGPEGAFLPPHQGFHRFLGIPYSHDQGPCQNLTCFPPDIPCKGGCDQGLVPIPLLANLTVEAQPPWLPGLEARYVSFSRDLMADAQRQGRPFFLYYASHHTHYPQFSGQSFTKRSGRGPFGDSLMELDGAVGALMTTVGDLGLLEETLVIFTADNGPELMRMSNGGCSGLLRCGKGTTFEGGVREPALVYWPGHITPGVTHELASSLDLLPTLAALTGAPLPNVTLDGVDISPLLLGTGKSPRKSVFFYPPYPDEIHGVFAVRNGKYKAHFFTQGSAHSDTTSDPACHAANRLTAHEPPLLYDLSQDPGENYNVLESIEGVSPEALQALKHIQLLKAQYDAAMTFGPSQIAKGEDPALQICCQPSCTPHPVCCHCPGSQS
Glycosylation Sites
Displaying all 4 entries
Position Description PubMed ID GlyTouCan ID Source
157
  • N-linked (GlcNAc...) asparagine
183
  • N-linked (GlcNAc...) asparagine
322
349
  • N-linked (GlcNAc...) asparagine
Feature
  • ProtVista GlyGen : Glycosylation Site from GlyGen
  • ProtVista UniProt : Glycosylation Site from UniProt
Pathway
Displaying all 3 entries
Pathway Name Organism
Glycosphingolipid catabolism Mus musculus
Neutrophil degranulation Mus musculus
The activation of arylsulfatases Mus musculus
Disease
Displaying 1 entry
DO ID Disease Name Source
DOID:10581 metachromatic leukodystrophy

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International Collaboration

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Acknowledgements

Supported by JST NBDC Grant Number JPMJND2204

Partly supported by NIH Common Fund Grant #1U01GM125267-01


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Last updated: April 6, 2026